SINGLE STAGE SURGICAL RELEASE OF LOWER LIMB CIRCUMFERENTIAL CONSTRICTION BAND IN A PATIENT WITH AMNIOTIC BAND SYNDROME: CASE REPORT

M. Busang, S. Gichuru, M. Svenning, D. Jowi, F. W. Nang’ole and D. A. Kulber

ABSTRACT

Overview
Amniotic Band Syndrome (ABS), also known as constriction band syndrome, is a congenital condition caused by fibrous bands originating from the amniotic sac. These bands can encircle a developing fetus during pregnancy and may lead to multiple deformities including constriction bands, acrosyndactyly, and limb amputations.

Circumferential constriction bands present a particular surgical challenge due to the potential risk of vascular compromise during release. For this reason, some literature recommends staged surgical release.

Case Presentation
This report presents the case of a 15 month old female with Amniotic Band Syndrome affecting all limbs, including a circumferential constriction band on the left leg.

Management and Outcome
The patient was successfully treated with a single stage surgical release using serial Z plasty.

Postoperative healing was excellent, with good palpable distal pulses and complete resolution of lymphedema.

Conclusion
This case illustrates the feasibility and safety of single stage circumferential release in patients with Amniotic Band Syndrome.